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Repeatability and reproducibility of the Forskolin-induced swelling (FIS) assay on intestinal organoids from people with Cystic Fibrosis.
Bierlaagh MC, Ramalho AS, Silva IAL, Vonk AM, van den Bor RM, van Mourik P, Pott J, Suen SWF, Boj SF, Vries RGJ, Lammertyn E, Vermeulen F, Amaral MD, de Boeck K, van der Ent CK, Beekman JM. Bierlaagh MC, et al. Among authors: van der ent ck. J Cyst Fibros. 2024 May 14:S1569-1993(24)00060-2. doi: 10.1016/j.jcf.2024.04.014. Online ahead of print. J Cyst Fibros. 2024. PMID: 38749892
Experimental, within-subject repeatability was also high within each lab (CCCs all >0.9). Longer-term repeatability (>1 year) showed more variability (CCCs from 0.67 to 0.95). ...
Experimental, within-subject repeatability was also high within each lab (CCCs all >0.9). Longer-term repeatability (>1 year) s …
Enhanced aortic stiffness in adolescents with chronic disease is associated with decreased left ventricular global longitudinal strain.
Verpalen VA, Ververs FA, Slieker M, Nuboer R, Swart JF, van der Ent CK, Fejzic Z, Westenberg JJM, Leiner T, Grotenhuis HB, Schipper HS. Verpalen VA, et al. Among authors: van der ent ck. Int J Cardiol Heart Vasc. 2024 Apr 26;52:101385. doi: 10.1016/j.ijcha.2024.101385. eCollection 2024 Jun. Int J Cardiol Heart Vasc. 2024. PMID: 38694268 Free PMC article.
Whether the decreased LVGLS in the chronic disease groups could negatively impact their long-term cardiovascular outcomes requires further study....
Whether the decreased LVGLS in the chronic disease groups could negatively impact their long-term cardiovascular outcomes requires fu …
Radiological and long-term clinical response to elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis with advanced lung disease.
Aalbers BL, Mohamed Hoesein FAA, Hofland RW, Bronsveld I, Kruijswijk MA, Schotman S, Slingerland CW, Panhuis H, van der Ent CK, Heijerman HGM. Aalbers BL, et al. Among authors: van der ent ck. Pediatr Pulmonol. 2023 Aug;58(8):2317-2322. doi: 10.1002/ppul.26486. Epub 2023 May 24. Pediatr Pulmonol. 2023. PMID: 37222401 Clinical Trial.
Evidence for Beneficial Effect of Daily Use of Mechanical Insufflation-Exsufflation in Patients With Neuromuscular Diseases.
Veldhoen ES, van der Wal R, Verweij-van den Oudenrijn LP, Wösten-van Asperen RM, Gaytant MA, van der Ent CK, van der Pol WL, Hulzebos EH. Veldhoen ES, et al. Among authors: van der ent ck. Respir Care. 2023 Apr;68(4):531-546. doi: 10.4187/respcare.09664. Respir Care. 2023. PMID: 36963967 Free PMC article. Review.
One randomized controlled trial (RCT) found a trend toward reduced duration of respiratory infections compared to air stacking (AS) that was not statistically significant. Long-term effects on pulmonary function tests (PFT) results were reported in one RCT and one retrospe …
One randomized controlled trial (RCT) found a trend toward reduced duration of respiratory infections compared to air stacking (AS) that was …
Long-term effectiveness of dual CFTR modulator treatment of cystic fibrosis.
Muilwijk D, Zomer-van Ommen DD, Gulmans VAM, Eijkemans MJC, van der Ent CK; Dutch Cystic Fibrosis Registry (NCFR) Steering Group:. Muilwijk D, et al. Among authors: van der ent ck. ERJ Open Res. 2022 Nov 14;8(4):00204-2022. doi: 10.1183/23120541.00204-2022. eCollection 2022 Oct. ERJ Open Res. 2022. PMID: 36382237 Free PMC article.
BACKGROUND: Although short-term efficacy of lumacaftor/ivacaftor and tezacaftor/ivacaftor is clearly established in clinical trials, data on long-term effectiveness is limited. ...Intravenous antibiotic treatment duration showed a three-fold reduction in the first y …
BACKGROUND: Although short-term efficacy of lumacaftor/ivacaftor and tezacaftor/ivacaftor is clearly established in clinical trials, …
VOCAL: An observational study of ivacaftor for people with cystic fibrosis and selected non-G551D-CFTR gating mutations.
Simmonds NJ, van der Ent CK, Colombo C, Kinnman N, DeSouza C, Thorat T, Chew ML, Chandarana K, Castellani C. Simmonds NJ, et al. Among authors: van der ent ck. J Cyst Fibros. 2023 Jan;22(1):124-131. doi: 10.1016/j.jcf.2022.05.007. Epub 2022 May 23. J Cyst Fibros. 2023. PMID: 35613999 Free article.
BACKGROUND: VOCAL was an observational study of the effect of long-term ivacaftor on real-world clinical outcomes and healthcare resource utilization (HCRU) in people with cystic fibrosis (pwCF) in Italy, the Netherlands, and the UK. ...Reported safety results were consist …
BACKGROUND: VOCAL was an observational study of the effect of long-term ivacaftor on real-world clinical outcomes and healthcare reso …
Natural history of respiratory muscle strength in spinal muscular atrophy: a prospective national cohort study.
Veldhoen ES, Wijngaarde CA, Hulzebos EHJ, Wösten-van Asperen RM, Wadman RI, van Eijk RPA, Asselman FL, Stam M, Otto LAM, Cuppen I, Scheijmans FEV, den Oudenrijn LPV, Bartels B, Gaytant MA, van der Ent CK, van der Pol WL. Veldhoen ES, et al. Among authors: van der ent ck. Orphanet J Rare Dis. 2022 Feb 21;17(1):70. doi: 10.1186/s13023-022-02227-7. Orphanet J Rare Dis. 2022. PMID: 35189949 Free PMC article.
These natural history data may serve as a reference for longer-term treatment efficacy assessments....
These natural history data may serve as a reference for longer-term treatment efficacy assessments....
Short-term effect and effect on rate of lung function decline after surgery for neuromuscular or syndromic scoliosis.
Veldhoen ES, de Vries A, Schlosser TPC, Kruyt MC, van Eijk RPA, Tersmette JM, Hulzebos EH, van der Pol LW, Wösten-van Asperen RM, van der Ent CK. Veldhoen ES, et al. Among authors: van der ent ck. Pediatr Pulmonol. 2022 May;57(5):1303-1309. doi: 10.1002/ppul.25857. Epub 2022 Feb 24. Pediatr Pulmonol. 2022. PMID: 35174667 Free PMC article.
Forskolin-induced organoid swelling is associated with long-term cystic fibrosis disease progression.
Muilwijk D, de Poel E, van Mourik P, Suen SWF, Vonk AM, Brunsveld JE, Kruisselbrink E, Oppelaar H, Hagemeijer MC, Berkers G, de Winter-de Groot KM, Heida-Michel S, Jans SR, van Panhuis H, van der Eerden MM, van der Meer R, Roukema J, Dompeling E, Weersink EJM, Koppelman GH, Vries R, Zomer-van Ommen DD, Eijkemans MJC, van der Ent CK, Beekman JM. Muilwijk D, et al. Among authors: van der ent ck. Eur Respir J. 2022 Aug 18;60(2):2100508. doi: 10.1183/13993003.00508-2021. Print 2022 Aug. Eur Respir J. 2022. PMID: 35086832 Free PMC article.
Here we assessed the association of forskolin-induced swelling (FIS) of patient-derived organoids with long-term CF disease progression in multiple organs and compared FIS with the golden standard biomarker sweat chloride concentration (SCC). ...We used linear mixed-effect …
Here we assessed the association of forskolin-induced swelling (FIS) of patient-derived organoids with long-term CF disease progressi …
Psychosocial functioning in adolescents growing up with chronic disease: The Dutch HBSC study.
Berkelbach van der Sprenkel EE, Nijhof SL, Dalmeijer GW, Onland-Moret NC, de Roos SA, Lesscher HMB, van de Putte EM, van der Ent CK, Finkenauer C, Stevens GWJM. Berkelbach van der Sprenkel EE, et al. Among authors: van der ent ck. Eur J Pediatr. 2022 Feb;181(2):763-773. doi: 10.1007/s00431-021-04268-9. Epub 2021 Sep 30. Eur J Pediatr. 2022. PMID: 34595612 Free PMC article. Review.
Participants indicated whether they or one of their family members had a long-term (> 3 months) disease or disability (mental/physical) and were categorized into four groups based on disease presence (none, other, self, both). ...What is Known: Adolescents who grow up w …
Participants indicated whether they or one of their family members had a long-term (> 3 months) disease or disability (mental/phys …
61 results