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31 results

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Page 1
Late Diagnosis in the Era of Universal Newborn Screening Negatively Affects Short- and Long-Term Growth and Health Outcomes in Infants with Cystic Fibrosis.
Martiniano SL, Wu R, Farrell PM, Ren CL, Sontag MK, Elbert A, McColley SA. Martiniano SL, et al. Among authors: farrell pm. J Pediatr. 2023 Nov;262:113595. doi: 10.1016/j.jpeds.2023.113595. Epub 2023 Jul 3. J Pediatr. 2023. PMID: 37406853
Through evaluation of national patient registry data, we determined that late initiation of cystic fibrosis care is associated with poorer long-term nutritional outcomes....
Through evaluation of national patient registry data, we determined that late initiation of cystic fibrosis care is associated with poorer l …
Newborn screening for cystic fibrosis. The Cystic Fibrosis Neonatal Screening Study Group.
Farrell PM, Mischler EH. Farrell PM, et al. Adv Pediatr. 1992;39:35-70. Adv Pediatr. 1992. PMID: 1442316 Review.
The major gap in knowledge that must be closed before CF neonatal screening can be recommended generally in the United States concerns the potential long-term medical benefits of initiating treatment in early infancy. It would be premature, in our opinion, to implement mas …
The major gap in knowledge that must be closed before CF neonatal screening can be recommended generally in the United States concerns the p …
Newborn screening alone insufficient to improve pulmonary outcomes for cystic fibrosis.
Barreda CB, Farrell PM, Laxova A, Eickhoff JC, Braun AT, Coller RJ, Rock MJ. Barreda CB, et al. Among authors: farrell pm. J Cyst Fibros. 2021 May;20(3):492-498. doi: 10.1016/j.jcf.2020.06.002. Epub 2020 Jun 13. J Cyst Fibros. 2021. PMID: 32546430 Free PMC article.
Because the evaluations of these subjects by protocol ended in 2012, our objective was to assess long-term pulmonary and mortality outcomes. METHODS: Retrospective analysis of the RCT cohort utilized longitudinal outcome measures obtained from the Cystic Fibrosis Foundatio …
Because the evaluations of these subjects by protocol ended in 2012, our objective was to assess long-term pulmonary and mortality ou …
Long-term follow-up of cystic fibrosis newborn screening: psychosocial functioning of adolescents and young adults.
Tluczek A, Laxova A, Grieve A, Heun A, Brown RL, Rock MJ, Gershan WM, Farrell PM. Tluczek A, et al. Among authors: farrell pm. J Cyst Fibros. 2014 Mar;13(2):227-34. doi: 10.1016/j.jcf.2013.10.001. Epub 2013 Oct 21. J Cyst Fibros. 2014. PMID: 24157354 Free PMC article.
BACKGROUND: Long-term psychosocial outcomes of cystic fibrosis (CF) patients diagnosed through newborn screening remain unknown. ...
BACKGROUND: Long-term psychosocial outcomes of cystic fibrosis (CF) patients diagnosed through newborn screening remain unknown. ...
Long-term evaluation of genetic counseling following false-positive newborn screen for cystic fibrosis.
Cavanagh L, Compton CJ, Tluczek A, Brown RL, Farrell PM. Cavanagh L, et al. Among authors: farrell pm. J Genet Couns. 2010 Apr;19(2):199-210. doi: 10.1007/s10897-009-9274-4. Epub 2010 Feb 4. J Genet Couns. 2010. PMID: 20131088 Free PMC article.
This cross-sectional mixed method study was a long-term follow-up evaluation of families who participated in an earlier survey of their understanding of cystic fibrosis (CF) genetics and their infants' false-positive CF newborn screening (NBS) results. ...Results showed pa …
This cross-sectional mixed method study was a long-term follow-up evaluation of families who participated in an earlier survey of the …
ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals.
De Wachter E, De Boeck K, Sermet-Gaudelus I, Simmonds NJ, Munck A, Naehrlich L, Barben J, Boyd C, Veen SJ, Carr SB, Fajac I, Farrell PM, Girodon E, Gonska T, Grody WW, Jain M, Jung A, Kerem E, Raraigh KS, van Koningsbruggen-Rietschel S, Waller MD, Southern KW, Castellani C; ECFS Diagnostic Network Working Group. De Wachter E, et al. Among authors: farrell pm. J Cyst Fibros. 2024 Feb 21:S1569-1993(24)00011-0. doi: 10.1016/j.jcf.2024.01.012. Online ahead of print. J Cyst Fibros. 2024. PMID: 38388234
Topics included are: 1) benefits and obstacles to collect data from pwCFTR-RD are discussed, together with the opportunity to integrate them into established CF-registries; 2) the potential of infants designated CRMS/CFSPID to develop a CFTR-RD and how to communicate this informa …
Topics included are: 1) benefits and obstacles to collect data from pwCFTR-RD are discussed, together with the opportunity to integrate them …
Pubertal Height Growth and Adult Height in Cystic Fibrosis After Newborn Screening.
Zhang Z, Lindstrom MJ, Farrell PM, Lai HJ; Wisconsin Cystic Fibrosis Neonatal Screening Group. Zhang Z, et al. Among authors: farrell pm. Pediatrics. 2016 May;137(5):e20152907. doi: 10.1542/peds.2015-2907. Epub 2016 Apr 5. Pediatrics. 2016. PMID: 27244789 Free PMC article. Clinical Trial.
BACKGROUND: To examine long-term growth benefit of newborn screening (NBS), adolescent peak height velocity (PHV), and adult height were compared between the screened (diagnosed early via NBS) and the control (identified generally by symptoms) in the Wisconsin Randomized C …
BACKGROUND: To examine long-term growth benefit of newborn screening (NBS), adolescent peak height velocity (PHV), and adult height w …
Poor recovery from cystic fibrosis pulmonary exacerbations is associated with poor long-term outcomes.
Sanders DB, Zhao Q, Li Z, Farrell PM. Sanders DB, et al. Among authors: farrell pm. Pediatr Pulmonol. 2017 Oct;52(10):1268-1275. doi: 10.1002/ppul.23765. Epub 2017 Sep 7. Pediatr Pulmonol. 2017. PMID: 28881091 Free PMC article.
RATIONALE: People with CF treated with IV antibiotics for a pulmonary exacerbation (PEx) frequently fail to recover to baseline FEV(1) . The long-term impact of these events has not been studied. OBJECTIVES: To determine if a patient's spirometric recovery after a PEx is a …
RATIONALE: People with CF treated with IV antibiotics for a pulmonary exacerbation (PEx) frequently fail to recover to baseline FEV(1) . The …
Risk of persistent growth impairment after alternate-day prednisone treatment in children with cystic fibrosis.
Lai HC, FitzSimmons SC, Allen DB, Kosorok MR, Rosenstein BJ, Campbell PW, Farrell PM. Lai HC, et al. Among authors: farrell pm. N Engl J Med. 2000 Mar 23;342(12):851-9. doi: 10.1056/NEJM200003233421204. N Engl J Med. 2000. PMID: 10727589 Free article. Clinical Trial.
BACKGROUND: It is uncertain whether the growth impairment that occurs in children during long-term treatment with glucocorticoids persists after the medication is discontinued and ultimately affects adult height. ...
BACKGROUND: It is uncertain whether the growth impairment that occurs in children during long-term treatment with glucocorticoids per …
Long-term mechanical ventilation in pediatric respiratory failure: medical and ethical considerations.
Farrell PM, Fost NC. Farrell PM, et al. Am Rev Respir Dis. 1989 Aug;140(2 Pt 2):S36-40. doi: 10.1164/ajrccm/140.2_Pt_2.S36. Am Rev Respir Dis. 1989. PMID: 2504092
Because the survival and quality of life for children receiving long-term assisted ventilation are not highly discouraging, increasing numbers of pediatric patients are not being managed at home with life-support technology. ...
Because the survival and quality of life for children receiving long-term assisted ventilation are not highly discouraging, increasin …
31 results