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ECFS standards of care on CFTR-related disorders: Towards a comprehensive program for affected individuals.
De Wachter E, De Boeck K, Sermet-Gaudelus I, Simmonds NJ, Munck A, Naehrlich L, Barben J, Boyd C, Veen SJ, Carr SB, Fajac I, Farrell PM, Girodon E, Gonska T, Grody WW, Jain M, Jung A, Kerem E, Raraigh KS, van Koningsbruggen-Rietschel S, Waller MD, Southern KW, Castellani C; ECFS Diagnostic Network Working Group. De Wachter E, et al. Among authors: castellani c. J Cyst Fibros. 2024 Feb 21:S1569-1993(24)00011-0. doi: 10.1016/j.jcf.2024.01.012. Online ahead of print. J Cyst Fibros. 2024. PMID: 38388234
Topics included are: 1) benefits and obstacles to collect data from pwCFTR-RD are discussed, together with the opportunity to integrate them into established CF-registries; 2) the potential of infants designated CRMS/CFSPID to develop a CFTR-RD and how to communicate this informa …
Topics included are: 1) benefits and obstacles to collect data from pwCFTR-RD are discussed, together with the opportunity to integrate them …
Short-term effects of positive expiratory pressure mask on ventilation inhomogeneity in children with cystic fibrosis: A randomized, sham-controlled crossover study.
Gambazza S, Mariani A, Guarise R, Ferrari B, Carta F, Brivio A, Bizzarri S, Castellani C, Colombo C, Laquintana D. Gambazza S, et al. Among authors: castellani c. Pediatr Pulmonol. 2024 Feb 16. doi: 10.1002/ppul.26915. Online ahead of print. Pediatr Pulmonol. 2024. PMID: 38362833
Measurement with the N(2) MBW and the crossover design were found to be time-consuming and unsuitable for a short-term study of airway clearance techniques....
Measurement with the N(2) MBW and the crossover design were found to be time-consuming and unsuitable for a short-term study of airwa …
Long-term motor activity, cardiopulmonary performance and quality of life in abdominal wall defect patients.
Flucher C, Windhaber J, Gasparella P, Castellani C, Tschauner S, Mittl B, Wolfschluckner V, Singer G, Till H. Flucher C, et al. Among authors: castellani c. Pediatr Res. 2024 Mar;95(4):1101-1109. doi: 10.1038/s41390-023-02900-y. Epub 2023 Dec 5. Pediatr Res. 2024. PMID: 38052863 Free PMC article.
AIM: To assess whether patients born with an abdominal wall defect (AWD) have impaired cardiorespiratory performance capacity, motor skills, core stability or quality of life in a long-term follow up. METHODS: Patients diagnosed with AWD between 2002 and 2013 were invited …
AIM: To assess whether patients born with an abdominal wall defect (AWD) have impaired cardiorespiratory performance capacity, motor skills, …
Vortex supersolid in the XY model with tunable vortex fugacity.
Maccari I, Defenu N, Castellani C, Enss T. Maccari I, et al. Among authors: castellani c. J Phys Condens Matter. 2023 May 18;35(33). doi: 10.1088/1361-648X/acd295. J Phys Condens Matter. 2023. PMID: 37141896
In this paper, we investigate the XY model in the presence of an additional potential term that independently tunes the vortex fugacity favouring their nucleation. By increasing the strength of this term and thereby the vortex chemical potential, we observe signific …
In this paper, we investigate the XY model in the presence of an additional potential term that independently tunes the vortex fugaci …
Effect of Dornase Alfa on the Lung Clearance Index in Children with Cystic Fibrosis: A Lesson from a Case Series.
Terlizzi V, Parisi GF, Ferrari B, Castellani C, Manti S, Leonardi S, Taccetti G. Terlizzi V, et al. Among authors: castellani c. Children (Basel). 2022 Oct 26;9(11):1625. doi: 10.3390/children9111625. Children (Basel). 2022. PMID: 36360353 Free PMC article.
In both centers, LCI was performed routinely, every 3-6 months, based on the clinical picture and severity of the lung disease. In this study, we evaluated the LCI before and after long-term DNase therapy. RESULTS: DNase improved LCI values in the absence of respiratory ex …
In both centers, LCI was performed routinely, every 3-6 months, based on the clinical picture and severity of the lung disease. In this stud …
[Italian Cystic Fibrosis Registry (ICFR). Report 2019-2020].
Campagna G, Amato A, Majo F, Ferrari G, Quattrucci S, Padoan R, Floridia G, Salvatore D, Carnovale V, Puppo Fornaro G, Taruscio D, Salvatore M; Gruppo di lavoro RIFC. Campagna G, et al. Epidemiol Prev. 2022 Jul-Aug;46(4 Suppl 2):1-38. doi: 10.19191/EP22.4S2.060. Epidemiol Prev. 2022. PMID: 36102313 Free article. Italian.
INTRODUCTION: Italian cystic fibrosis registry (ICFR) collects data from cystic fibrosis (CF) patients through the collaboration with Italian CF referral and support Centres (Italian law 548/93). ICFR contributes: to the analysis of medium and long term clinical and epidem …
INTRODUCTION: Italian cystic fibrosis registry (ICFR) collects data from cystic fibrosis (CF) patients through the collaboration with Italia …
VOCAL: An observational study of ivacaftor for people with cystic fibrosis and selected non-G551D-CFTR gating mutations.
Simmonds NJ, van der Ent CK, Colombo C, Kinnman N, DeSouza C, Thorat T, Chew ML, Chandarana K, Castellani C. Simmonds NJ, et al. Among authors: castellani c. J Cyst Fibros. 2023 Jan;22(1):124-131. doi: 10.1016/j.jcf.2022.05.007. Epub 2022 May 23. J Cyst Fibros. 2023. PMID: 35613999 Free article.
BACKGROUND: VOCAL was an observational study of the effect of long-term ivacaftor on real-world clinical outcomes and healthcare resource utilization (HCRU) in people with cystic fibrosis (pwCF) in Italy, the Netherlands, and the UK. ...Reported safety results were consist …
BACKGROUND: VOCAL was an observational study of the effect of long-term ivacaftor on real-world clinical outcomes and healthcare reso …
Marginal versus Standard Donors in Heart Transplantation: Proper Selection Means Heart Transplant Benefit.
Bifulco O, Bottio T, Caraffa R, Carrozzini M, Guariento A, Bejko J, Fedrigo M, Castellani C, Toscano G, Lorenzoni G, Tarzia V, Gregori D, Cardillo M, Puoti F, Feltrin G, Angelini A, Gerosa G. Bifulco O, et al. Among authors: castellani c. J Clin Med. 2022 May 9;11(9):2665. doi: 10.3390/jcm11092665. J Clin Med. 2022. PMID: 35566789 Free PMC article.
BACKGROUND: In this study, we assessed the mid-term outcomes of patients who received a heart donation from a marginal donor (MD), and compared them with those who received an organ from a standard donor (SD). METHODS: All patients who underwent HTx between January 2012 an …
BACKGROUND: In this study, we assessed the mid-term outcomes of patients who received a heart donation from a marginal donor (MD), an …
Clinical outcomes of a large cohort of individuals with the F508del/5T;TG12 CFTR genotype.
Tosco A, Castaldo A, Colombo C, Claut L, Carnovale V, Iacotucci P, Lucarelli M, Cimino G, Fabrizzi B, Caporelli N, Majo F, Ciciriello F, Padoan R, Poli P, Taccetti G, Centrone C, Casciaro R, Castellani C, Salvatore D, Colangelo C, Bonomi P, Castaldo G, Terlizzi V. Tosco A, et al. Among authors: castellani c. J Cyst Fibros. 2022 Sep;21(5):850-855. doi: 10.1016/j.jcf.2022.04.020. Epub 2022 May 4. J Cyst Fibros. 2022. PMID: 35523714
BACKGROUND: In recent years, patients with cystic fibrosis (CF) conductance regulator (CFTR) variant poly(T) sequences have been increasingly reported with a wide spectrum of clinical severity. We describe the long-term clinical outcomes and progression to a CF diagnosis o …
BACKGROUND: In recent years, patients with cystic fibrosis (CF) conductance regulator (CFTR) variant poly(T) sequences have been increasingl …
44 results