Cystic fibrosis, pancreatic sufficiency and distal intestinal obstruction syndrome: a report of four cases

Acta Paediatr. 1995 May;84(5):577-8. doi: 10.1111/j.1651-2227.1995.tb13699.x.

Abstract

Distal intestinal obstruction syndrome (DIOS), formerly termed meconium ileus equivalent, is usually considered to be unique to cystic fibrosis (CF) patients who have steatorrhoea. We report four CF patients without steatorrhoea ("pancreatic sufficient") who have had repeated episodes of faecal loading indistinguishable from DIOS.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Child, Preschool
  • Cystic Fibrosis / complications*
  • Feces / chemistry
  • Female
  • Humans
  • Infant
  • Intestinal Obstruction / complications*
  • Lipids / analysis
  • Male
  • Pancreatic Diseases / complications*
  • Syndrome

Substances

  • Lipids