Improvement in bronchiectasis on CT imaging in a pediatric patient with cystic fibrosis on ivacaftor therapy

Respiration. 2014;88(4):345. doi: 10.1159/000365999. Epub 2014 Aug 21.
No abstract available

Publication types

  • Case Reports

MeSH terms

  • Aminophenols / administration & dosage*
  • Bronchiectasis* / diagnostic imaging
  • Bronchiectasis* / etiology
  • Child
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / drug therapy
  • Cystic Fibrosis* / genetics
  • Cystic Fibrosis* / physiopathology
  • Drug Monitoring / methods
  • Female
  • Humans
  • Membrane Transport Modulators / administration & dosage
  • Quinolones / administration & dosage*
  • Spirometry / methods
  • Tomography, X-Ray Computed / methods
  • Treatment Outcome

Substances

  • Aminophenols
  • CFTR protein, human
  • Membrane Transport Modulators
  • Quinolones
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • ivacaftor