Aquagenic wrinkling of the palms in a patient with cystic fibrosis

N Engl J Med. 2013 Dec 12;369(24):2362-3. doi: 10.1056/NEJMc1308349.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Aminophenols / pharmacology*
  • Aminophenols / therapeutic use
  • Child
  • Chlorides / analysis
  • Cystic Fibrosis / complications
  • Cystic Fibrosis / drug therapy*
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis Transmembrane Conductance Regulator / physiology*
  • Genotype
  • Hand
  • Humans
  • Male
  • Quinolones / pharmacology*
  • Quinolones / therapeutic use
  • Skin Aging / drug effects*
  • Sweat / chemistry
  • Water

Substances

  • Aminophenols
  • CFTR protein, human
  • Chlorides
  • Quinolones
  • Water
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • ivacaftor